HUMAN DISEASE PHENOTYPE | CFTR KNOCKOUT MOUSE MODEL PHENOTYPE | TIUKO CF RAT PHENOTYPE |
---|---|---|
LUNG FIBROSIS | FIBROSIS AND INFLAMMATION | PRESENT BY 100 DAYS OF AGE |
MRP8/14 ELEVATED | DETECTED IN G551D MOUSE | INCREASED PRENATALLY |
AIRWAY REACTIVITY | NOT DETECTED | INCREASED WITH AGE |
CHRONIC INFLAMMATION | DETECTED IN CONGENIC MICE | PRESENT BY 100 DAYS OF AGE |